Pulmonary arterial hypertension in patients with systemic sclerosis

Protsenko G.O.¹, Sirenko Yu.M.²

• ¹State Institution National Scientific Center «Institute of Cardiology named after acad. M.D. Strazheska» National Academy of Medical Sciences of Ukraine
• ²ДУ «Національний науковий центр «Інститут кардіології ім. М.Д. Стражеска» НАМН України», Київ

Summary. Pulmonary arterial hypertension (PAH) in patients with systemic sclerosis (SSc) is widely known as severe manifestation of connective tissue disease, rapid progression of which leads to adverse consequences. Different course and prognosis of the disease, as well as a therapeutic strategy requires careful differential diagnosis with other lung diseases. Early diagnosis of PАH requires the application of modern instrumental methods that are available in the major specialized medical-diagnostic centers of Ukraine.